Kitzsteiner K A, Mallen R G
Cancer. 1980 Nov 15;46(10):2248-9. doi: 10.1002/1097-0142(19801115)46:10<2248::aid-cncr2820461022>3.0.co;2-5.
Pulmonary lymphangiomyomatosis (PLM) is a rare disease of smooth muscle proliferation that generally leads to an early death due to respiratory insufficiency. The disease only affects women. Exacerbations with pregnancy and after hormonal manipulation have been documented. There is presently no successful treatment of the disease. Castration as a means of early therapy has been associated with a stable respiratory picture in our patient. Peritoneal-jugular shunt can benefit women with significant ascities.
肺淋巴管平滑肌瘤病（PLM）是一种平滑肌增殖的罕见疾病，通常因呼吸功能不全导致早期死亡。该疾病仅影响女性。已有文献记载妊娠及激素治疗后病情会加重。目前该疾病尚无成功的治疗方法。在我们的患者中，阉割作为早期治疗手段与呼吸状况稳定相关。颈静脉分流术可使有大量腹水的女性受益。
