Oxorn D C, Landrigan P
Department of Anaesthesia, Halifax Infirmary, N.S.
Can J Anaesth. 1987 Sep;34(5):512-4. doi: 10.1007/BF03014360.
Pulmonary lymphangiomyomatosis is an idiopathic disease, resulting in severe respiratory impairment. Bilateral oophorectomy has led to objective and subjective amelioration of the pulmonary pathology. In the anaesthetic management of such a patient, careful attention must be paid to pulmonary and systemic haemodynamics, and gas exchange. We describe the successful anaesthetic management of a 34-year-old female, using epidural anaesthesia, and pulmonary artery catheterization. Although the intraoperative and immediate postoperative courses were heralded by marked cardiorespiratory stability, refractory respiratory failure developed, and she died five months after surgery.
肺淋巴管平滑肌瘤病是一种特发性疾病，可导致严重的呼吸功能损害。双侧卵巢切除术已使肺部病变在客观和主观上得到改善。对于此类患者的麻醉管理，必须密切关注肺和全身血流动力学以及气体交换。我们描述了一名34岁女性患者成功的麻醉管理过程，采用了硬膜外麻醉和肺动脉导管插入术。尽管术中及术后即刻过程表现为显著的心、肺稳定性，但仍出现了难治性呼吸衰竭，患者在术后五个月死亡。
