Kehoe R F, Bauernfeind R, Tommaso C, Wyndham C, Rosen K M
Ann Intern Med. 1981 Jan;94(1):41-3. doi: 10.7326/0003-4819-94-1-41.
The clinical electrophysiologic findings in four patients with biopsy-proven polymyositis and bifascicular block are described. Atrioventricular (AV) block developed in two of these four patients, and intracardiac electrophysiologic studies documented the site of spontaneous block to be distal to the His bundle in one, whereas in the second marked His-ventricular prolongation was found, and distal block developed at low paced atrial rates. Sinus node and AV nodal function were normal in all four. These electrophysiologic data provide the first documentation of the site of AV block in patients with polymyositis and correlate well with findings of previous pathologic studies that have shown extensive fibrosis of the distal His bundle and bundle branches.
本文描述了4例经活检证实为多发性肌炎且伴有双分支阻滞患者的临床电生理检查结果。这4例患者中有2例发生了房室（AV）阻滞，心内电生理研究显示，其中1例患者自发阻滞的部位在希氏束远端，而另一例患者则发现希氏束至心室的间期显著延长，且在低心房起搏频率时出现远端阻滞。4例患者的窦房结和房室结功能均正常。这些电生理数据首次记录了多发性肌炎患者房室阻滞的部位，与既往病理研究结果高度相关，既往病理研究显示希氏束远端和束支存在广泛纤维化。
