De Wilde F, D'Haens M, Smet H, Martin J J, Tassignon M J
Department of Ophthalmology, University Hospital of Antwerp.
Bull Soc Belge Ophtalmol. 1995;255:139-46.
We describe the surgical approach of two patients with myogenic blepharoptosis. The ptosis is caused by a glycogenosis type II (Pompe disease) in the first case and is due to a juvenile, chronic progressive external ophthalmoplegia (Kearns-Sayre syndrome) in the second case. The first patient presented a unilateral ptosis. The ptosis in the second patient was bilateral and manifest. The eyelids could only be opened manually. A resection of the palpebral levator muscle was carried out under local anesthesia. The choice of the technique will be explained. The amount of levator resection was calculated considering the residual eyelid motility and Bell's phenomenon. Electronmicroscopy of the resected levator muscle will be discussed.
我们描述了两名患有肌源性上睑下垂患者的手术方法。第一例患者的上睑下垂由II型糖原贮积病（庞贝病）引起，第二例患者的上睑下垂则是由于青少年慢性进行性外眼肌麻痹（卡恩斯-塞尔综合征）。第一例患者表现为单侧上睑下垂。第二例患者的上睑下垂为双侧且明显，眼睑只能手动睁开。在局部麻醉下进行了睑提肌切除术，并将对该技术的选择进行解释。根据残余眼睑活动度和贝尔现象计算睑提肌切除量。还将讨论切除的睑提肌的电子显微镜检查结果。
