Watanabe A, Yanagita M, Ishii R, Shirabe T
Department of Neurosurgery, Kawasaki Medical School, Okayama.
Neurol Med Chir (Tokyo). 1994 Jul;34(7):448-50. doi: 10.2176/nmc.34.448.
A rare case of ecchordosis physaliphora clearly demonstrated by magnetic resonance (MR) imaging is described in a 48-year-old male who presented with right hearing disturbance and reduction in sensation in the right side of his face due to a large cystic schwannoma. MR imaging revealed the large cystic schwannoma as well as an abnormal clival lesion. The clival lesion was hypointense on T1-weighted images and hyperintense on T2-weighted images, and not enhanced by gadolinium-diethylenetriamine-penta-acetic acid (Gd-DTPA) administration. The clival lesion was partially removed. The histological diagnosis was ecchordosis physaliphora. The postoperative course was uneventful. The absence of enhancement of ecchordosis physaliphora by Gd-DTPA administration may be a characteristic finding, in contrast to chordoma which is generally enhanced.
本文描述了一例通过磁共振成像（MR）清晰显示的罕见的泡状脊索瘤病例，患者为一名48岁男性，因巨大囊性神经鞘瘤出现右耳听力障碍及右侧面部感觉减退。MR成像显示出巨大囊性神经鞘瘤以及斜坡异常病变。斜坡病变在T1加权图像上呈低信号，在T2加权图像上呈高信号，注射钆喷酸葡胺（Gd-DTPA）后无强化。斜坡病变被部分切除。组织学诊断为泡状脊索瘤。术后病程平稳。与通常有强化表现的脊索瘤不同，泡状脊索瘤注射Gd-DTPA后无强化可能是其特征性表现。
