Griffin A C, Zhao W, Wegmann K W, Hickley W F
Department of Pathology, Dartmouth Medical School, Lebanon, New Hampshire 03756, USA.
Am J Pathol. 1995 Sep;147(3):845-57.
Type I diabetes, an autoimmune disease that occurs in humans and animals, is characterized by the destruction of insulin-secreting islet beta-cells of the pancreas. Antibodies directed toward multiple islet protein can be detected before diagnosis of type I diabetes; however, the identity of the inciting autoantigen(s) that targets beta-cells for destruction has not been defined. Autorecognition of many self-proteins by CD4+ T lymphocytes is restricted by the products of class II immune response genes of the major histocompatibility complex (MHC), and in human type I diabetes such a MHC association has been described. The present study uses a rat MHC class II (RT1.Bl) peptide binding motif to predict potentially autoreactive CD4+ T cell epitopes in two key islet beta-cell constituents: the enzyme glutamic acid decarboxylase (GAD) and the insulin precursor hormone proinsulin (PI). Seventeen-amino-acid-long peptide fragments of GAD and PI containing the binding motif were synthesized and used to generate peptide-specific, MHC class II-restricted, CD4+ T cell lines. Once established, the T cell lines specific for rat islet GAD and PI were adoptively transferred to naive, MHC-compatible rats. At 10 days after transfer, insulitis had developed in rats receiving PI-specific T cells, whereas no insulitis was observed in pancreata of rats receiving GAD-specific T cells. Of particular interest is the finding that the pathogenic T cell epitope identified in PI spans the endogenous cleavage site between the B-chain and C-peptide of insulin. Moreover, the PI-specific T cells were able to react specifically with material produced in vitro by a rat insulinoma cell line. These results demonstrate that pathogenic T cell epitopes can be located in portions of molecules that are subsequently degraded during normal enzymatic processing. As PI is found highest concentrations in the beta-cells of pancreatic islets, it is possible that this molecule and not its individual degradation products (ie, insulin and C-peptide) might serve as an autoantigen in the pathogenesis of type I diabetes.
1型糖尿病是一种发生于人类和动物的自身免疫性疾病,其特征是胰腺中分泌胰岛素的胰岛β细胞被破坏。在1型糖尿病诊断之前就能检测到针对多种胰岛蛋白的抗体;然而,靶向β细胞进行破坏的引发自身抗原的身份尚未明确。CD4 + T淋巴细胞对许多自身蛋白的自身识别受主要组织相容性复合体(MHC)II类免疫反应基因产物的限制,并且在人类1型糖尿病中已经描述了这种MHC关联。本研究使用大鼠MHC II类(RT1.Bl)肽结合基序来预测两种关键的胰岛β细胞成分中潜在的自身反应性CD4 + T细胞表位:酶谷氨酸脱羧酶(GAD)和胰岛素前体激素胰岛素原(PI)。合成了包含该结合基序的GAD和PI的17个氨基酸长的肽片段,并用于产生肽特异性、MHC II类限制的CD4 + T细胞系。一旦建立,将对大鼠胰岛GAD和PI特异的T细胞系过继转移到未接触过抗原、MHC相容的大鼠。转移后10天,接受PI特异性T细胞的大鼠发生了胰岛炎,而接受GAD特异性T细胞的大鼠胰腺中未观察到胰岛炎。特别有趣的是在PI中鉴定出的致病T细胞表位跨越了胰岛素B链和C肽之间的内源性切割位点。此外,PI特异性T细胞能够与大鼠胰岛素瘤细胞系体外产生的物质特异性反应。这些结果表明,致病T细胞表位可以位于在正常酶促加工过程中随后被降解的分子部分中。由于PI在胰岛β细胞中浓度最高,因此该分子而非其单个降解产物(即胰岛素和C肽)可能在1型糖尿病发病机制中作为自身抗原。