一例合并法洛四联症及左心室憩室的坎特雷尔五联症

[A case of pentalogy of Cantrell with tetralogy of Fallot and left ventricular diverticulum].

作者信息

Fukazawa M, Orita H, Hirooka S, Uchino H, Washio M, Akiba T

机构信息

Second Department of Surgery, Yamagata University School of Medicine, Japan.

出版信息

Kyobu Geka. 1995 Aug;48(9):759-62.

PMID:7564038

Abstract

We report a successful repair of tetralogy of Fallot and left ventricular diverticulum associated with pentaology of Cantrell. The repair consisted of partial infundibular septectomy, closure of ventricular septum, reconstruction of right ventricular outlet using monocuspid transjunctional patch, and resection of left ventricular diverticulum. The infundibulum was extremely elongated, caused by ventricular dextroversion, and the hypoplasia of pulmonary trunk was absent. Therefore, transjunctional patch was longer, even after infundibular septectomy. This report discuss the pathogenesis of these cardiac anomalies and surgical imlication.

摘要

我们报告了一例法洛四联症合并左心室憩室及坎特雷尔五联症的成功修复病例。修复手术包括部分漏斗间隔切除术、室间隔闭合、使用单尖瓣跨交界补片重建右心室流出道以及切除左心室憩室。漏斗部因心室右旋而极度延长，且肺动脉干无发育不全。因此，即使在漏斗间隔切除术后，跨交界补片仍较长。本报告讨论了这些心脏异常的发病机制及手术意义。