Sipahier M
Department of Pediatric Dentistry, University of Gazi, Faculty of Dentistry, Ankara, Turkey.
Quintessence Int. 1994 Dec;25(12):839-43.
The term epidermolysis bullosa describes a group of rare genetic mechanicobullous disorders. The disease has several modes of inheritance with various degrees of severity and expression. A patient with simplex epidermolysis bullosa had typical cutaneous lesions and dental involvement. The teeth were severely affected by hypoplasia. Dental therapy consisted of placement of amalgam restorations and topical applications of fluoride. The need for, and advantages of, early preventive and restorative dental care are illustrated by the case presented.
大疱性表皮松解症这一术语描述了一组罕见的遗传性机械性大疱性疾病。该疾病有多种遗传模式,严重程度和表现各不相同。一名单纯型大疱性表皮松解症患者有典型的皮肤病变和牙齿受累情况。牙齿受到严重的发育不全影响。牙科治疗包括放置汞合金修复体和局部应用氟化物。所呈现的病例说明了早期预防性和修复性牙科护理的必要性及优势。