Adelaide Nursing School, Faculty of Health and Medical Sciences, The University of Adelaide, Adelaide, SA, Australia.
Australian Research Centre for Population Oral Health, School of Dentistry, The University of Adelaide, Adelaide, SA, Australia.
BMC Oral Health. 2024 Sep 27;24(1):1131. doi: 10.1186/s12903-024-04861-y.
Epidermolysis Bullosa (EB) is a genetic condition with fragility of the skin and oral mucosal lining requiring appropriate care and management by dental health professionals. The objective of this scoping review was to comprehensively examine the specialised dental needs of children with Epidermolysis Bullosa and map evidence towards the type, availability, and accessibility of specialised dental care services within various health care systems.
This scoping review was conducted using the JBI Methodology framework for scoping reviews. Five databases were used to source relevant literature: MEDLINE, Embase, Dentistry & Oral Sciences Source, Scopus, and Web of Science during the period 1963-2022.
Thirty three published case reports were identified reporting on 45 participants encompassing the dental care and management of children diagnosed with EB aged between 0-12 years of age from an Australian and international health care context. The findings reveal the need for greater awareness amongst health professionals in the management and specialised dental care needs of children and the need for further research, and care pathways for children with EB.
There is a dearth of evidence which examines the dental needs of children, in particular referral pathways and timely access to dental health services and professionals. Dentists play an important role in monitoring and providing individualised and specialised oral care and treatment to the child with EB. It is vital that dentists as well as the wider multidisciplinary team have knowledge and understanding of the EB condition in meeting the specialised needs and management of these children.
大疱性表皮松解症（EB）是一种遗传性疾病，皮肤和口腔黏膜脆弱，需要牙科专业人员提供适当的护理和管理。本研究旨在全面评估患有大疱性表皮松解症儿童的特殊牙科需求，并绘制证据，以了解各种医疗保健系统中特殊牙科护理服务的类型、可及性和可及性。
本研究采用 JBI 方法学框架进行范围综述。在 1963 年至 2022 年期间，使用了五个数据库来获取相关文献：MEDLINE、Embase、Dentistry & Oral Sciences Source、Scopus 和 Web of Science。
确定了 33 篇已发表的病例报告，报告了 45 名参与者，涵盖了澳大利亚和国际医疗保健背景下诊断为 EB 的 0-12 岁儿童的牙科护理和管理。研究结果表明，需要提高卫生专业人员对儿童管理和特殊牙科护理需求的认识，需要进一步研究和为 EB 儿童制定护理途径。
缺乏专门针对儿童牙科需求的证据，特别是转诊途径和及时获得牙科保健服务和专业人员的途径。牙医在监测和为 EB 儿童提供个性化和特殊口腔护理和治疗方面发挥着重要作用。牙医以及更广泛的多学科团队了解 EB 病情对于满足这些儿童的特殊需求和管理至关重要。
