Cottalorda J, Jouve J L, Bollini G, Brehier P, Daoud A, Muracciole P, Toth C
Service de Chirurgie Infantile, Hôpital Nord, Saint-Etienne.
Rev Chir Orthop Reparatrice Appar Mot. 1995;81(1):74-7.
The clinical features of two children with myositis ossificans progressiva are described. Skeletal malformations can be observed in many sites: hand, femur, tibia and spine. Phalangeal abnormalities (shortened hallux, hallux valgus) are essential to the diagnosis. We recommend systematic roentgenographic examination to search for other skeletal malformations for congenital hallux valgus in young children because it can be the first sign of myositis ossificans progressiva. Progression of disability does not seem to be influenced by any form of medical treatment. Surgical removal of ectopic bone is thought to be followed inevitably by rapid recalcification at the original site.
本文描述了两名进行性骨化性肌炎患儿的临床特征。在许多部位可观察到骨骼畸形：手部、股骨、胫骨和脊柱。指骨异常（拇趾缩短、拇外翻）对诊断至关重要。我们建议对幼儿先天性拇外翻进行系统的X线检查，以寻找其他骨骼畸形，因为这可能是进行性骨化性肌炎的首发症状。残疾的进展似乎不受任何形式的药物治疗影响。异位骨的手术切除被认为不可避免地会导致原部位迅速重新钙化。
