新生儿狼疮综合征：一例报告
Neonatal lupus syndrome: report of a case.
作者信息
Gürakan B, Yalçin S, Tekinalp G, Celiker A
机构信息
Department of Pediatrics, Hacettepe University Faculty of Medicine, Ankara.
出版信息
Turk J Pediatr. 1995 Apr-Jun;37(2):153-6.
Neonatal lupus syndrome (NLS) is characterized by the presence of cutaneous lupus, congenital heart block or both associated with maternal autoantibodies anti-Ro (SS-A) and anti-La (SS-B). NLS is responsible for more than 80 percent of cases with isolated congenital complete heart block. This report describes a neonate with third-degree atrioventricular block who was born to an anti-Ro (SS-A) positive mother. The dermatological and hematological manifestations of NLS were absent. The infant's clinical condition was good during the two months of follow-up with expectant management.
新生儿狼疮综合征（NLS）的特征是存在皮肤狼疮、先天性心脏传导阻滞或两者兼有，且与母体抗Ro（SS-A）和抗La（SS-B）自身抗体相关。NLS是孤立性先天性完全性心脏传导阻滞病例中80%以上的病因。本报告描述了一名患有三度房室传导阻滞的新生儿，其母亲抗Ro（SS-A）呈阳性。该患儿无NLS的皮肤和血液学表现。在两个月的随访观察期内，患儿临床状况良好。
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