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系统性红斑狼疮和疱疹样皮炎:与马方综合征并发。

Systemic lupus erythematosus and dermatitis herpetiformis: concurrence with Marfan's syndrome.

作者信息

Aronson A J, Soltani K, Aronson I K, Ong R T

出版信息

Arch Dermatol. 1979 Jan;115(1):68-70.

PMID:760661
Abstract

There is increasing evidence that, as in systemic lupus erythematosus (SLE), deposition of immune complexes plays a role in the pathogenesis of dermatitis herpetiformis (DH). Dermatitis herpetiformis and SLE were diagnosed in a 15-year-old girl with Marfan's syndrome who died of cardiac tamponade secondary to cystic medial necrosis of the ascending aorta. The concurrence of these diseases suggests that predisposition to immune-mediated disorders may be associated with the expression of multiple clinical entities.

摘要

越来越多的证据表明,与系统性红斑狼疮(SLE)一样,免疫复合物的沉积在疱疹样皮炎(DH)的发病机制中起作用。一名患有马凡综合征的15岁女孩被诊断出患有疱疹样皮炎和系统性红斑狼疮,该女孩死于升主动脉囊性中层坏死继发的心包填塞。这些疾病的同时出现表明,免疫介导疾病的易感性可能与多种临床实体的表现有关。

相似文献

1
Systemic lupus erythematosus and dermatitis herpetiformis: concurrence with Marfan's syndrome.系统性红斑狼疮和疱疹样皮炎:与马方综合征并发。
Arch Dermatol. 1979 Jan;115(1):68-70.
2
Concurrence of lupus erythematosus and dermatitis herpetiformis. A report of nine cases.
Arch Dermatol. 1983 Sep;119(9):740-5.
3
IgA-containing circulating immune complexes in dermatitis herpetiformis, Henoch-Schönlein purpura, systemic lupus erythematosus and other diseases.疱疹样皮炎、过敏性紫癜、系统性红斑狼疮及其他疾病中含IgA的循环免疫复合物
Clin Exp Immunol. 1980 Jun;40(3):431-7.
4
The association of dermatitis herpetiformis and systemic lupus erythematosus.疱疹样皮炎与系统性红斑狼疮的相关性。
J Am Acad Dermatol. 2010 Nov;63(5):892-5. doi: 10.1016/j.jaad.2009.05.037. Epub 2010 Aug 23.
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Simultaneous systemic lupus erythematosus and dermatitis herpetiformis.
Arch Dermatol. 1976 Sep;112(9):1292-4.
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[Dermatitis herpetiformis and systemic lupus erythematosus].
Med Cutan Ibero Lat Am. 1984;12(4):311-7.
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Diseases associated with dermatitis herpetiformis.与疱疹样皮炎相关的疾病。
Br J Dermatol. 1997 Mar;136(3):315-8.
8
[Diagnostic problems associated with the coincidence of bullous dermatosis and lupus erythematosus visceralis. Demonstration of a case with Duhring's dermatitis herpetiformis in association with visceral lupus erythematosus].[大疱性皮肤病与内脏红斑狼疮并存时的诊断问题。1例疱疹样皮炎(杜林病)合并内脏红斑狼疮的病例展示]
Dermatologica. 1976;153(1):57-64.
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[A case of Duhring's dermatitis in systemic lupus erythematosus: associated disease or simulated disease].
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Dermatitis herpetiformis--a skin manifestation of a generalized disturbance in immunity.
Q J Med. 1978 Apr;47(186):221-48.

引用本文的文献

1
Castleman disease and SLE in a G6PD-deficient Marfan patient: a case report and literature review.葡萄糖-6-磷酸脱氢酶缺乏的马凡综合征患者合并卡斯特曼病和系统性红斑狼疮:一例报告及文献综述
Auto Immun Highlights. 2020 Nov 3;11(1):16. doi: 10.1186/s13317-020-00138-w.
2
Dermatitis herpetiformis and rheumatoid arthritis.疱疹样皮炎与类风湿关节炎。
Ann Rheum Dis. 1979 Aug;38(4):399. doi: 10.1136/ard.38.4.399-b.