Chiaretti A, Scommegna S, Castorina M, Piastra M, Tortorolo L, Villani A, Polidori G
Istituto di Clinica Pediatrica, Università Catolica Sacro Cuore di Roma, Italia.
Pediatr Med Chir. 1995 Mar-Apr;17(2):177-9.
Henoch-Schoenlein syndrome (HSS) is one of the most common vasculitis in childhood. It is characterized by non-thrombocytopenic purpura, arthritis, abdominal pain, and sometimes intestinal haemorrhage and renal involvement. It may be complicated by haemorrhages in uncommon sites, such as lungs, testicles, bladder, and central nervous system. Neurological involvement in HSS is often underestimated, usually occurring with headache, irritability, and behavioural alterations, whereas endocranial haemorrhage is quite rare. We report a case of endocranial haemorrhage in a child with HSS.
亨诺-许兰综合征(HSS)是儿童期最常见的血管炎之一。其特征为非血小板减少性紫癜、关节炎、腹痛,有时还会出现肠道出血和肾脏受累。它可能会并发于肺部、睾丸、膀胱和中枢神经系统等不常见部位的出血。HSS的神经受累情况常常被低估,通常表现为头痛、易怒和行为改变,而颅内出血则相当罕见。我们报告一例患有HSS的儿童发生颅内出血的病例。