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成人先天性脐尿管未闭:一例报告

Congenital patent urachus in an adult: a case report.

作者信息

Takano Y, Okatani K, Okamoto S, Enoki N

机构信息

Department of Urology, Okatani Hospital, Nara, Japan.

出版信息

Int J Urol. 1994 Sep;1(3):275-7. doi: 10.1111/j.1442-2042.1994.tb00050.x.

DOI:10.1111/j.1442-2042.1994.tb00050.x
PMID:7614387
Abstract

A rare case of the congenital patent urachus in an adult is reported. The patient, a 42-year-old man, was admitted with the chief complaint of macroscopic hematuria. During the cystoscopy perfusion water discharged from the umbilicus. Diagnostic imaging revealed a tubular fistula between the bladder and umbilicus and the patient underwent urachal resection and partial cystectomy. Microscopically the lumen was lined by transitional, columnar and squamous epithelium and there was no evidence of malignancy. To date 11 cases of congenital patent urachus in an adult have been reported in Japan. From a review of the Japanese literature, the common chief complaint is urine discharge from the umbilicus accompanying cystitis and/or urachal inflammation. Urachal resection is performed in all cases. We also clarified the epithelial histology of the patent urachus in this patient.

摘要

报告了一例成人先天性脐尿管未闭的罕见病例。患者为一名42岁男性,因肉眼血尿为主诉入院。膀胱镜检查时,灌注的水从脐部流出。诊断性影像学检查显示膀胱与脐部之间存在管状瘘,患者接受了脐尿管切除术和部分膀胱切除术。显微镜下,管腔内衬有移行上皮、柱状上皮和鳞状上皮,无恶性证据。迄今为止,日本已报告11例成人先天性脐尿管未闭病例。通过回顾日本文献,常见的主要症状是伴有膀胱炎和/或脐尿管炎症的脐部尿液排出。所有病例均进行了脐尿管切除术。我们还明确了该患者未闭脐尿管的上皮组织学特征。

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Congenital patent urachus in an adult: a case report.成人先天性脐尿管未闭:一例报告
Int J Urol. 1994 Sep;1(3):275-7. doi: 10.1111/j.1442-2042.1994.tb00050.x.
2
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