Shiraki K, Takase K, Tameda Y, Kosaka Y
First Department of Internal Medicine, Mie University School of Medicine.
Nihon Rinsho. 1995 Jun;53(6):1479-83.
Pancreatic involvement associated with acute intermittent porphyria is rare. There were only nine cases reported until now which have pancreatic disease and AIP, one case with chronic pancreatitis, one with cystadenocarcinoma and chronic pancreatitis, one with transient macroamylasemia and the others with acute pancreatitis. The cause of these complications in these patients is uncertain. However, in our case, it is possible that AIP might have caused the acute pancreatitis, since this patient developed acute pancreatitis following the attack of AIP. It seems to be necessary to pay attention to the combination of these diseases.
与急性间歇性卟啉症相关的胰腺受累情况罕见。截至目前,仅有9例报告同时患有胰腺疾病和急性间歇性卟啉症,其中1例为慢性胰腺炎,1例为囊腺癌合并慢性胰腺炎,1例为短暂性巨淀粉酶血症,其他病例为急性胰腺炎。这些患者出现这些并发症的原因尚不确定。然而,在我们的病例中,急性间歇性卟啉症可能导致了急性胰腺炎,因为该患者在急性间歇性卟啉症发作后出现了急性胰腺炎。似乎有必要关注这些疾病的合并情况。