Tucci D L, Telian S A, Zimmerman-Phillips S, Zwolan T A, Kileny P R
Department of Surgery, Duke University Medical Center, Durham, NC, USA.
Arch Otolaryngol Head Neck Surg. 1995 Aug;121(8):833-8. doi: 10.1001/archotol.1995.01890080005001.
To report operative findings, postoperative course, and postimplantation performance in patients with cochlear malformations who underwent cochlear implantation.
Case study and intervention study (before-after trial). Minimum follow-up of 12 months; average follow-up of 24 months.
Academic tertiary referral center.
Six patients, including five children who underwent implantation at ages 3.5 to 13 years and one adult who underwent implantation at age 27 years. malformations included common cavity deformity (n = 1), cochlear hypoplasia (n = 2), and incomplete partition (n = 3). All patients with cochlear malformations who underwent implantation at the University of Michigan, Ann Arbor, are included, selected from a group of 196 patients so treated since 1986.
Implantation with a standard multichannel cochlear implant.
Operative findings described include round window and facial nerve anatomy and cerebrospinal fluid leak. Postoperative roentgenographic findings, electrode activation, and reason for non-use of electrodes were investigated. Standard tests of speech perception were used to compare preoperative and postoperative performance for each subject.
Operative findings included round window abnormalities (three patients), anomalous facial nerve (one patient), and cerebrospinal fluid leak (three patients). No surgical complications occurred. A minimum of 10 electrodes were activated for all patients. Electrode thresholds and discomfort levels were variable for several months after implantation. All patients demonstrated improved performance after implantation. Four subjects demonstrated open-set speech perception. Two other subjects, whose poor language skills precluded administration of standard tests, showed increased awareness of environmental sounds and increased vocalization after implantation.
Cochlear implantation can be a successful method of rehabilitation in patients with congenital deafness who have cochlear malformations.
报告接受人工耳蜗植入的耳蜗畸形患者的手术发现、术后病程及植入后的表现。
病例研究和干预研究（前后试验）。最短随访12个月；平均随访24个月。
学术性三级转诊中心。
6例患者，包括5名年龄在3.5至13岁接受植入的儿童和1名27岁接受植入的成人。畸形包括共同腔畸形（n = 1）、耳蜗发育不全（n = 2）和不完全分隔（n = 3）。纳入了所有在密歇根大学安娜堡分校接受植入的耳蜗畸形患者，这些患者选自1986年以来接受此类治疗的196例患者。
植入标准多通道人工耳蜗。
描述的手术发现包括圆窗和面神经解剖结构以及脑脊液漏。调查术后影像学检查结果、电极激活情况及未使用电极的原因。使用标准言语感知测试比较每个受试者术前和术后的表现。
手术发现包括圆窗异常（3例患者）、面神经异常（1例患者）和脑脊液漏（3例患者）。未发生手术并发症。所有患者至少激活了10个电极。植入后数月，电极阈值和不适水平各不相同。所有患者植入后表现均有所改善。4名受试者表现出开放式言语感知。另外2名受试者由于语言能力差无法进行标准测试，植入后对环境声音的意识增强且发声增加。
人工耳蜗植入对于患有耳蜗畸形的先天性耳聋患者可能是一种成功的康复方法。
