Department of Otorhinolaryngology, Çukurova University Faculty of Medicine, Adana, Turkey.
J Int Adv Otol. 2022 May;18(3):203-209. doi: 10.5152/iao.2022.20134.
Cochlear implants are arguably the most successful neural prosthesis today. Cochlear implantation has several difficulties in patients with internal ear anomalies. This study was performed to analyze intraoperative, postoperative findings, and auditory performance of 55 patients who had inner ear malformations and were treated with cochlear implants at Otorhinolaryngology Department of Çukurova University Hospital.
Auditory performances were analyzed in 30 of 55 patients. Patients with cochlear anomalies were evaluated as group I, patients with vestibular malformation as group II, and patients with the normal bone labyrinth as group III. Listening progress profiles and meaningful auditory integration scale tests were used to determine performances.
Comparison between the listening progress profiles test performance of the groups at 12th and 18th month of group I was significantly lower than other groups (P < .05) and reached at the same level after the 24th month. Comparison between the meaningful auditory integration scale test performance of groups at 24th and 36th month of group I was significantly lower than other groups (P < .05). Perilymph gusher was observed in 3 patients who had incomplete partition I malformation. Oozing was observed in 50% of incomplete partition II patients. Facial nerve traced a variant course in 4 of 55 patients and 6 patients had postoperative meningitis.
Initially patients with inner ear anomalies showed that the level of language development was worse than patients with normal bone anatomy. However, it was shown that they both reached the same point as a result. Facial nerve anomaly and meningitis risk is higher in patients with inner ear malformations.
人工耳蜗植入术可以说是当今最成功的神经假体之一。对于内耳畸形的患者，人工耳蜗植入术存在若干困难。本研究旨在分析在库尤大学医院耳鼻喉科接受人工耳蜗植入术的 55 例内耳畸形患者的术中、术后发现和听觉表现。
对 55 例患者中的 30 例进行了听觉表现分析。将耳蜗畸形患者评估为 I 组，前庭畸形患者评估为 II 组，正常骨迷路患者评估为 III 组。使用听力进展概况和有意义的听觉整合量表测试来确定患者的听觉表现。
与其他两组相比，I 组患者在第 12 个月和第 18 个月的听力进展概况测试表现明显较低（P <.05），但在第 24 个月后达到相同水平。与其他两组相比，I 组患者在第 24 个月和第 36 个月的有意义听觉整合量表测试表现明显较低（P <.05）。3 例不完全分隔 I 畸形患者出现外淋巴漏，50%的不完全分隔 II 患者出现渗液。4 例患者面神经走行异常，6 例患者术后发生脑膜炎。
最初，内耳畸形患者的语言发育水平较正常骨解剖患者差，但结果表明两者最终达到相同水平。内耳畸形患者面神经异常和脑膜炎的风险较高。
