大脑大静脉动静脉瘤。一项临床、血管造影CT扫描及神经病理学研究。

Arteriovenous aneurysm of the vein of Galen. A clinical, angiographic CT scan and neuropathological study.

作者信息

Iannucci A M, Buonanno F, Rizzuto N, Mazza C, Vivenza C, Maschio A

出版信息

J Neurol Sci. 1979 Jan;40(1):29-37. doi: 10.1016/0022-510x(79)90006-6.

Abstract

An autopsied case of arteriovenous aneurysm of the vein of Galen in a 31/2-month-old female is reported. Arteriovenous aneurysm of the vein of Galen is a rare vascular malformation of the central nervous system consisting of a saccular dilatation of the vein which receives blood shunted through enlarged arteries. These peculiar structural and hemodynamic characteristics differentiate this particular malformation from the other AVMs of the central nervous system. In infants the arteriovenous aneurysm of the vein of Galen is characterized clinically by hydrocephalus and cardiomegaly. In the present paper the clinical features and diagnostic indications are discussed and, in particular, the role of computerized cranial tomography (CT) is emphasized as a rapid and noninvasive procedure for detection of intracranial disorders.

摘要

报告了一例3个半月大女性的大脑大静脉动静脉瘤尸检病例。大脑大静脉动静脉瘤是一种罕见的中枢神经系统血管畸形，由静脉的囊状扩张组成，该静脉接收通过扩大的动脉分流的血液。这些独特的结构和血流动力学特征使这种特殊的畸形与中枢神经系统的其他动静脉畸形区分开来。在婴儿中，大脑大静脉动静脉瘤的临床特征是脑积水和心脏肥大。本文讨论了其临床特征和诊断指征，尤其强调了计算机断层扫描（CT）作为一种快速、无创检测颅内疾病的方法的作用。