Gel'fand V B, Adamian A A, Boĭmuradov O S
Khirurgiia (Mosk). 1995(3):42-3.
The authors had 21 patients with a rare disease, Madelung's lipomatosis. Vegetative disorders of segmental and suprasegmental levels were revealed in all patients. The character of neuropathies in Madelung's lipomatosis is discussed in detail. According to the authors, it is a complex syndrome with peripheral, vegetative, and vascular disorders. The accompanying secondary scalenus syndrome produces a peculiar clinical picture of neuropathy. The existence of neurological disorders dictates the need for complex (surgical and medicamentous) treatment of patients with Madelung's lipomatosis.
作者有21例患有罕见疾病——马德隆脂肪过多症的患者。在所有患者中均发现了节段性和节段以上水平的自主神经功能障碍。文中详细讨论了马德隆脂肪过多症中神经病变的特征。据作者称,这是一种伴有周围、自主神经和血管功能障碍的复杂综合征。伴随的继发性斜角肌综合征产生了一种特殊的神经病变临床表现。神经功能障碍的存在表明需要对马德隆脂肪过多症患者进行综合(手术和药物)治疗。