Matamala Gimeno C, Pérez Calvo J I, Rodríguez Benavente A M, Moros M, Pérez Villaroya J C, Bueno Gómez J
Servicio de Medicina Interna B, Hospital Clínico Universitario, Zaragoza.
An Med Interna. 1995 Mar;12(3):127-9.
We present a case of multiple symmetric lipomatosis Type I (Madelung's disease) with severe organic affection, hepatic cirrhosis, sever sensitive polyneuropathy and neuropathic ulceration at the left lower limb. A nephrotic syndrome developed in a larval form due to proliferative glomerulonephritis as the result of a metainfectious complications of the infection at the lower limb. We discuss the etiopathogenicity of the organic affection and we highlight the pathogenic links between the disease and its complications.
我们报告一例I型多发性对称性脂肪瘤病（马德隆病），伴有严重器官损害、肝硬化、严重感觉性多神经病以及左下肢神经病理性溃疡。由于下肢感染的感染后并发症导致增殖性肾小球肾炎，进而出现幼虫型肾病综合征。我们讨论了器官损害的病因，并强调了该疾病与其并发症之间的致病联系。
