Freixinet J, Sanchez-Palacios M, Guerrero D, Rodriguez de Castro F, Gonzalez D, Lopez L, Guerra M
Department of Thoracic Surgery, Hospital Insular de Gran Canaria, Canary Islands, Spain.
Scand J Thorac Cardiovasc Surg. 1995;29(1):39-41. doi: 10.3109/14017439509107200.
Congenital pulmonary arteriovenous fistula is frequently associated with hereditary haemorrhagic telangiectasia (Rendu-Osler-Weber disease). With the increased blood flow in pregnancy such fistulas enlarge, occasionally giving rise to haemothorax, which generally has a poor prognosis. A familial case is presented in which massive haemothorax required emergency thoracotomy in the 27th week of pregnancy.
先天性肺动静脉瘘常与遗传性出血性毛细血管扩张症（伦杜-奥斯勒-韦伯病）相关。妊娠期间随着血流量增加，此类瘘管会扩大，偶尔会引发血胸，其预后通常较差。本文报告了一例家族性病例，患者在妊娠第27周时因大量血胸需要紧急开胸手术。
