Iwabuchi S, Horikoshi A, Okada S, Tanita T, Fujimura S
Department of Surgery, Tohoku University, Sendai, Japan.
Surg Today. 1993;23(5):468-70. doi: 10.1007/BF00309510.
We report herein a rare case of a 21-year-old man with Rendu-Osler-Weber disease, otherwise known as hemorrhagic teleangiectasia, in whom a spontaneous hemothorax occurred following the rupture of one of multiple pulmonary arteriovenous fistulae (PAVF). An emergency life-saving operation was performed which revealed the ruptured fistula lying just beneath the visceral pleura. This case demonstrates that patients in whom a pulmonary angiogram shows an arteriovenous fistula lying just beneath the visceral pleura should undergo prophylactic surgery to avoid a life-threatening emergency, whenever possible.
我们在此报告一例罕见病例，一名21岁男性患有遗传性出血性毛细血管扩张症（又称伦杜-奥氏病），其多个肺动静脉瘘（PAVF）之一破裂后发生了自发性血胸。进行了紧急救命手术，术中发现破裂的瘘位于脏层胸膜下方。该病例表明，肺血管造影显示动静脉瘘位于脏层胸膜下方的患者，应尽可能接受预防性手术，以避免危及生命的紧急情况。
