[Intravascular lymphomatosis. Report of a case and brief review of the disease].

Intravascular lymphomatosis (IL), previously called "malignant angioendotheliomatosis", is a rare neoplastic disease in which mononuclear cells, of demonstrated lymphoid origin, proliferate in small blood vessels lumen. Any organ may be involved, standing out general status affectation, skin and central nervous system (CNS) because their frequency. A case of this disease is reported, who presented general impairment with prolonged fever, abdominal pain and cutaneous arborescent telangiectasias as the most significant clinical data. It become fatal in a short time. It was clinically considered to be a sepsis and diagnosis was only obtained in post-mortem study. This study revealed multiple organ infiltration by this neoplasm, with the notable exception of CNS. Immunohistochemical study confirmed the lymphoid origin of neoplastic cells. The main characteristics of IL are reviewed.