Pintér A, Farkas A, Jainsch M, Hock A, Hrabovszky Z
Pécsi Orvostudományi Egyetem, Gyermekgyógyászati Klinika.
Orv Hetil. 1995 Aug 27;136(35):1897-901.
The relative rarity of urogenital sinus and cloacal anomalies, the wide range of their anatomical variants furthermore the number of different surgical options makes the successful management of a child with such urogenital abnormality one of the greatest challenges to the paediatric surgeon. Based on their own experience and the literature the authors give a review of embryology, pathology, and diagnosis of urogenital sinus and cloacal abnormality. They detail the new surgical therapy developed by Hendren and Pena which has been adopted in their routine. This therapy has significantly improved the functional outcome and prognosis of these anomalies. Over the past 20 years 25 patients with urogenital sinus and cloacal abnormalities were surgically treated in the author's institute.
泌尿生殖窦和泄殖腔畸形相对少见，其解剖变异范围广泛，而且手术选择多样，这使得成功治疗患有此类泌尿生殖系统异常的儿童成为小儿外科医生面临的最大挑战之一。基于自身经验和文献，作者对泌尿生殖窦和泄殖腔畸形的胚胎学、病理学及诊断进行了综述。他们详细介绍了亨德伦和佩尼亚开发并已应用于日常工作中的新手术疗法。这种疗法显著改善了这些畸形的功能结局和预后。在过去20年里，作者所在机构对25例患有泌尿生殖窦和泄殖腔畸形的患者进行了手术治疗。
