Tangen J M, Haaland A
Avdeling for blodsykdommer, Ullevål sykehus, Oslo.
Tidsskr Nor Laegeforen. 1995 Aug 30;115(20):2535-7.
The idiopathic hypereosinophilic syndrome is a disorder characterized by sustained overproduction of eosinophils with undetectable etiology in addition to specific organ damage. Multiple organ systems may be involved in this condition, including the heart, lungs, skin and nervous system. The most important cause of mortality is myocardial involvement combined with valvular insufficiency. However, the prognosis for these patients has been to a large extent improved by greater awareness of this condition, combined with better surgical techniques. We describe two cases that illustrate the complex clinical situations that may be encountered in these patients.
特发性嗜酸性粒细胞增多综合征是一种以嗜酸性粒细胞持续过度产生且病因不明为特征的疾病,同时伴有特定器官损害。该病症可能累及多个器官系统,包括心脏、肺、皮肤和神经系统。死亡的最重要原因是心肌受累合并瓣膜功能不全。然而,通过对这种病症的更多认识以及更好的外科技术,这些患者的预后已在很大程度上得到改善。我们描述了两例病例,以说明这些患者可能遇到的复杂临床情况。