Storek J, Glaspy J A, Grody W W, Susi E, Slater E D
Department of Medicine, UCLA School of Medicine.
Am J Hematol. 1993 Jun;43(2):139-43. doi: 10.1002/ajh.2830430213.
A 45-year-old female with a long history of HLA-B27-positive ankylosing spondylitis and ulcerative colitis developed cyclic neutropenia. She was hospitalized for high fever during each of three consecutive episodes of absolute neutropenia. On the third hospitalization, granulocyte-colony-stimulating factor (G-CSF), 5 micrograms/kg/day, was given by subcutaneous injection and resulted in an increase of absolute neutrophil count from 0 to 2.2 x 10(9)/liter and an associated decrease of platelet count and hemoglobin as well as severe bone and joint pain predominantly in the middle and lower back and purulent diarrhea. The back pain necessitated discontinuation of the drug. Oral cyclosporine therapy was begun, and although the neutrophil count continued to oscillate, both the peaks and the nadirs were higher than previously, and symptoms of neutropenia subsided. We conclude that cyclosporine can be an effective treatment for cyclic neutropenia associated with autoimmunity since G-CSF may cause exacerbations of autoimmune disorders.
一名45岁女性,有长期HLA - B27阳性强直性脊柱炎和溃疡性结肠炎病史,发生了周期性中性粒细胞减少症。在连续三次绝对中性粒细胞减少发作期间,她每次都因高热住院。第三次住院时,皮下注射粒细胞集落刺激因子(G - CSF),剂量为5微克/千克/天,结果绝对中性粒细胞计数从0增加到2.2×10⁹/升,同时血小板计数和血红蛋白下降,并且主要在中下背部出现严重的骨和关节疼痛以及脓性腹泻。背痛使得药物不得不停用。开始口服环孢素治疗,尽管中性粒细胞计数仍有波动,但峰值和谷值均高于之前,中性粒细胞减少的症状也消退了。我们得出结论,由于G - CSF可能会加重自身免疫性疾病,环孢素可以作为治疗与自身免疫相关的周期性中性粒细胞减少症的有效疗法。