促纤维增生性婴儿型节细胞胶质瘤——病例报告

Desmoplastic infantile ganglioglioma--case report.

作者信息

Aida T, Abe H, Itoh T, Nagashima K, Inoue K

机构信息

Department of Neurosurgery, Hokkaido University School of Medicine, Sapporo.

出版信息

Neurol Med Chir (Tokyo). 1993 Jul;33(7):463-6. doi: 10.2176/nmc.33.463.

DOI:10.2176/nmc.33.463

PMID:7692325

Abstract

A desmoplastic infantile ganglioglioma occurred in a 5-month-old boy, manifesting as delayed psychomotor development. Computed tomography showed a large cystic mass involving the left occipitoparietal lobes. The tumor was totally removed. He has survived for 13 years without tumor recurrence. Histological examination disclosed marked desmoplasia intermixed with mature-looking ganglion cells, neoplastic glial cells, and small, immature round cells. These clinical and histological features enabled the diagnosis of desmoplastic infantile ganglioglioma.

摘要

一名5个月大的男婴发生了促纤维增生性婴儿型节细胞胶质瘤，表现为精神运动发育迟缓。计算机断层扫描显示一个巨大的囊性肿块累及左枕顶叶。肿瘤被完全切除。他已存活13年，无肿瘤复发。组织学检查发现明显的促纤维增生，其间混有外观成熟的神经节细胞、肿瘤性胶质细胞和小的未成熟圆形细胞。这些临床和组织学特征有助于诊断促纤维增生性婴儿型节细胞胶质瘤。