Renault F, Flores-Guevara R, D'Allest A M
Laboratoire de Neurophysiologie Clinique de l'Enfant, Hôpital Armand-Trousseau, Paris, France.
Dev Med Child Neurol. 1995 Apr;37(4):354-61. doi: 10.1111/j.1469-8749.1995.tb12013.x.
Segmental spinal myoclonus (SSM) involving a child's lower limb revealed the presence of a spinal cord tumour from T8 to T12. The clinical and electrophysiological features of SSM-during the child's development were studied. The presence of this disorder at two months of age did not disturb the development of walking, but did lead to orthopaedic complications. Four electromyographic recordings performed between 23 months and 7 years 10 months of age revealed the topographical extension of the SSM, its passage to rhythmicity, variable frequency and change in the sequence of activation of the muscles. These electroclinical features enable discussion of the pathophysiology of SSM by reference to neonatal motor automatisms and spinal generators.
累及儿童下肢的节段性脊髓肌阵挛（SSM）显示存在T8至T12的脊髓肿瘤。研究了该儿童发育过程中SSM的临床和电生理特征。该疾病在两个月大时出现并未干扰行走发育，但确实导致了骨科并发症。在23个月至7岁10个月期间进行的四次肌电图记录显示了SSM的地形扩展、其向节律性的转变、频率变化以及肌肉激活顺序的改变。这些电临床特征有助于通过参考新生儿运动自动症和脊髓发生器来讨论SSM的病理生理学。
