Perrault J
Division of Gastroenterology, Mayo Clinic, Rochester, Minnesota.
Gastroenterol Clin North Am. 1994 Dec;23(4):743-52.
Hereditary pancreatitis is a clinical condition in which typical pancreatitis is associated with an inheritance pattern strongly suggestive of an autosomal dominant trait. Different variants have been described, some with aminoaciduria and some with ductal anomalies. Recurrent attacks are typical and lead to complications more often than in the idiopathic variety. Pancreatic enzyme supplements or antioxidants may help reduce the frequency and/or severity of attacks.
遗传性胰腺炎是一种临床病症,典型的胰腺炎与强烈提示常染色体显性性状的遗传模式相关。已描述了不同的变异型,一些伴有氨基酸尿,一些伴有导管异常。反复发作是其典型特征,并且比特发性胰腺炎更常导致并发症。补充胰酶或使用抗氧化剂可能有助于减少发作的频率和/或严重程度。