Hanip M R, Isa M R, Zainudin B M
Department of Medicine, Universiti Kebangsaan Malaysia, Kuala Lumpur.
Singapore Med J. 1994 Oct;35(5):535-7.
A young East Malaysian lady presented with haemoptysis in 1989. Since then she had recurrent episodes of dyspnoea and two occasions of respiratory failure requiring assisted ventilation. An open lung biopsy showed intra-alveolar haemorrhage with diffuse interstitial fibrosis consistent with idiopathic pulmonary haemosiderosis after excluding secondary causes of pulmonary haemorrhage. She failed to respond to corticosteroid and continued to depend on oxygen until she succumbed to the illness 2 years after the presentation.
1989年,一名东马来西亚年轻女性出现咯血症状。从那时起,她反复出现呼吸困难,并有两次呼吸衰竭,需要辅助通气。排除肺出血的继发原因后,开胸肺活检显示肺泡内出血伴弥漫性间质纤维化,符合特发性肺含铁血黄素沉着症。她对皮质类固醇治疗无反应,持续依赖氧气,直至发病2年后病逝。