Joos H, Frick J, Wessely K, Rittinger O, Moritz E, Dietze O, Galvan G
Department of Urology, General Hospital, Salzburg, Austria.
Eur Urol. 1994;26(4):344-6. doi: 10.1159/000475413.
Klinefelter's syndrome with karyotype 47,XXY in patients with primary extragonadal germ cell tumors rarely occurs. The endocrinology of Klinefelter's syndrome is changed; elevated beta-human choriomic gonadotropin levels are present. Chemotherapy and thoracic surgery brought complete remission in a patient with lung metastases.
原发性性腺外生殖细胞肿瘤患者中核型为47,XXY的克兰费尔特综合征很少见。克兰费尔特综合征的内分泌发生改变;β-人绒毛膜促性腺激素水平升高。化疗和胸外科手术使一名有肺转移的患者完全缓解。