Yu B
PUMC Hospital, CAMS, Beijing.
Zhongguo Yi Xue Ke Xue Yuan Xue Bao. 1994 Oct;16(5):394-6.
This paper reports nine patients with the classic cutaneous findings of dermatomyositis who did not develop clinical or laboratory evidence of muscle disease for at least 2 years after onset of their skin manifestations. Such patients represent 3.5% of our total experience with dermatomyositis patients during a 12 years period. None of the patients had evidence of malignancy. Each of five patients treated with oral prednisone for their cutaneous lesion or mild myositis after onset of their skin manifestations 3-12 years and had marked improvement. The author emphasizes that the cutaneous manifestations of dermatomyositis are pathognomonic of this disease and the term of this disease proposes cutaneous type dermatomyositis better than amyopathic dermatomyositis.
本文报告了9例具有皮肌炎典型皮肤表现的患者,这些患者在皮肤表现出现后至少2年未出现肌肉疾病的临床或实验室证据。此类患者占我们12年期间皮肌炎患者总病例数的3.5%。所有患者均无恶性肿瘤证据。5例患者在皮肤表现出现3 - 12年后因皮肤病变或轻度肌炎接受口服泼尼松治疗,病情均有显著改善。作者强调,皮肌炎的皮肤表现是该疾病的特征性表现,用皮肤型皮肌炎这一术语比无肌病性皮肌炎更合适。