Fornadley J A, Seibert D J, Ostrov B E, Warren W S
Division of Otolaryngology, Head and Neck Surgery, Pennsylvania State University, College of Medicine, Milton S. Hershey Medical Center, Children's Hospital, University Hospital, Hershey 17033, USA.
Int J Pediatr Otorhinolaryngol. 1995 Jan;31(1):101-7. doi: 10.1016/0165-5876(94)01068-9.
Relapsing polychondritis (RP), while relatively rare, presents a characteristic clinical picture. Based upon a symptom complex of auricular, nasal, and respiratory chondritis associated with ocular and otic complaints, diagnosis can frequently be made with confidence in the absence of histologic confirmation. We present a case where a therapeutic intervention was required without sufficient criteria for diagnosis. Magnetic resonance imaging (MRI) proved useful in initial evaluation and allowed follow-up imaging demonstrating a gratifying response to steroid treatment. We believe that MRI has an important role in the diagnosis and subsequent evaluation of patients with proven or suspected RP, particularly those with tracheal involvement.
复发性多软骨炎(RP)虽然相对罕见,但呈现出特征性的临床表现。基于耳、鼻和呼吸道软骨炎的症状复合体,并伴有眼部和耳部症状,在缺乏组织学证实的情况下,通常也能自信地做出诊断。我们报告一例在没有足够诊断标准的情况下需要进行治疗干预的病例。磁共振成像(MRI)在初始评估中被证明是有用的,并能进行随访成像,显示出对类固醇治疗的良好反应。我们认为,MRI在已证实或疑似RP患者的诊断及后续评估中具有重要作用,尤其是那些有气管受累的患者。