Adams E M, Plotz P H
National Institute of Arthritis and Musculoskeletal and Skin Diseases, National Institutes of Health, Bethesda, Maryland, USA.
Rheum Dis Clin North Am. 1995 Feb;21(1):179-202.
Idiopathic inflammatory myopathies, polymyositis, dermatomyositis, and inclusion body myositis, are increasingly recognized to cause long-term disability in certain subsets of patients. Because these diseases are infrequent, only retrospective analysis of most treatments are available. In this article, identification of subsets of patients with different prognoses and discussion of confounding factors for increasing weakness are emphasized. The advantages and disadvantages of different therapies for myositis and for extraskeletal muscle features are also discussed.
特发性炎性肌病,如多发性肌炎、皮肌炎和包涵体肌炎,越来越被认为会在某些亚组患者中导致长期残疾。由于这些疾病并不常见,大多数治疗方法只能进行回顾性分析。在本文中,重点强调了识别不同预后的患者亚组以及讨论导致肌无力加重的混杂因素。同时也讨论了针对肌炎和骨骼外肌肉特征的不同治疗方法的优缺点。