Scheye T, Vanneuville G, Dechelotte P, Queroy-Malamenaide C, Aufauvre B
Service de Chirurgie Pédiatrique, Hôtel-Dieu, Clermont-Ferrand.
Ann Chir. 1995;49(1):47-55.
Duplications of the gastro intestinal tract are characterised (Ladd and Gross) by the following histological features two muscular layers with myenteric cells inside. Cystic or tubular, they are always situated on the mesenteric border of the gastro intestinal tract with a common blood supply. The pathogenesis of duplication affects early fetal development via various mechanisms. Located anywhere along the alimentary tract as in our review of 12 cases, clinical manifestations vary according to the site. Abdominal cystic mass, mediastinal compression or intestinal obstruction bleeding or perforation are possible symptoms, but the presentation is very variable. The age of presentation is usually within the first year of life. The diagnosis can be made preoperatively by several investigations but the malformation is frequently discovered during surgery. Surgery is the only treatment for these duplications, but smaller cystic lesions are easily treated. However surgery of extensive duplications remains difficult.
胃肠道重复畸形具有以下组织学特征（拉德和格罗斯）：有两层肌肉，内部有肌间细胞。呈囊性或管状，总是位于胃肠道的肠系膜缘，有共同的血液供应。重复畸形的发病机制通过多种机制影响胎儿早期发育。如我们对12例病例的回顾所示，其可位于消化道的任何部位，临床表现因部位而异。腹部囊性肿块、纵隔压迫、肠梗阻、出血或穿孔都可能是症状，但表现差异很大。发病年龄通常在出生后第一年。术前可通过多种检查做出诊断，但这种畸形常在手术中才被发现。手术是这些重复畸形的唯一治疗方法，但较小的囊性病变易于治疗。然而，广泛重复畸形的手术仍然困难。
