Price A J, Compson J P, Calonje E
Soft Tissue Tumours Unit, St Thomas' Hospital, London, UK.
J Hand Surg Br. 1995 Feb;20(1):16-8. doi: 10.1016/s0266-7681(05)80007-5.
Fibrolipomatous hamartoma of nerve is a rare benign infiltrating condition of peripheral nerves leading to progressive functional loss. Previous descriptions have virtually all been confined to the distal part of the upper limb, with the median nerve being the commonest reported site. Most cases occur in the first 3 decades of life and a third are associated with macrodactyly. A case is described in a 63-year-old woman, involving the whole of the brachial plexus, a previously unreported site for this particular lesion.
神经纤维脂肪瘤性错构瘤是一种罕见的良性周围神经浸润性疾病，可导致进行性功能丧失。以往的描述几乎都局限于上肢远端，正中神经是最常报道的部位。大多数病例发生在生命的前三十年，三分之一与巨指畸形有关。本文描述了一例63岁女性患者，病变累及整个臂丛神经，这是该特殊病变以前未报道过的部位。
