Murray R A, Poulton T B, Saltarelli M G, Dweik R A, Litwin D K, Kirby T J, Meziane M A, O'Donovan P B
Department of Diagnostic Radiology, Cleveland Clinic Foundation, Ohio, USA.
J Thorac Imaging. 1995 Spring;10(2):138-41. doi: 10.1097/00005382-199521000-00012.
Ehlers-Danlos syndrome (EDS) is an inherited disorder of connective tissue with multiple thoracic manifestations. We present an unusual thoracic manifestation of EDS consisting of parenchymal cysts and fibrous and fibroosseous nodules. These manifestations may be related to an abnormal attempt at repair of parenchymal or vascular tears.
埃勒斯-当洛综合征(EDS)是一种遗传性结缔组织疾病,有多种胸部表现。我们报告了一例EDS不寻常的胸部表现,包括实质囊肿以及纤维性和纤维骨性结节。这些表现可能与实质或血管撕裂修复的异常尝试有关。