Bakouche P, Ferroir J P, Guillard A
Service de Neurologie, Hôpital Tenon, Paris.
Rev Neurol (Paris). 1994 Oct;150(10):728-31.
Over a period of 10 years, a 49-year-old man had 3 episodes of recurrent cranial nerve palsy regressing within a few weeks. Each episode was accompanied with acute inaugural headache and diplopia and once with sensory impairment of the trigeminal nerf and once with tinnitus. The diagnosis of Goujerot-Sjögren's syndrome was retained after demonstration of hypergammaglobulinaemia, a positive Rose Bengale test and histological examination of biopsy specimens from the accessory salivary glands which revealed advanced typical lesions. Clinically, impaired secretion was not obvious.
在10年的时间里,一名49岁男性出现了3次复发性颅神经麻痹,每次发作在几周内自行缓解。每次发作都伴有急性起病的头痛和复视,一次伴有三叉神经感觉障碍,一次伴有耳鸣。在证实有高球蛋白血症、玫瑰红试验阳性以及对副唾液腺活检标本进行组织学检查发现典型的晚期病变后,确诊为干燥综合征。临床上,分泌功能受损并不明显。