Hochberg J, Ardenghy M F, Gustafson R A, Murray G F
Section of Plastic Surgery, West Virginia University, Morgantown.
Plast Reconstr Surg. 1995 Jan;95(1):148-51. doi: 10.1097/00006534-199501000-00026.
Thoracoabdominal ectopia cordis is a congenital malposition of the heart and abdominal viscera, which are externally situated, carrying an extremely poor prognosis. We report a case of a complete thoracoabdominal ectopia cordis that had undergone successful coverage over the exposed heart and abdominal contents. A few hours after birth, the defect was repaired with an expanded polytetrafluoroethylene soft-tissue patch that was gradually reduced by suture plication. Coverage was completed 48 hours later with bilateral pectoralis major and rectus abdominis myocutaneous flaps. Intraoperative tissue expansion minimized the cardiac compression produced by surgical reconstruction of the defect. Our patient, who is now 36 months old, represents the seventeenth case to survive reconstructive attempts.
胸腹型心脏异位是一种心脏和腹部脏器的先天性位置异常，这些脏器位于体外，预后极差。我们报告一例完全性胸腹型心脏异位病例，其外露的心脏和腹部脏器已成功覆盖。出生后数小时，用一块膨体聚四氟乙烯软组织补片修复缺损，通过缝线折叠逐渐缩小补片。48小时后用双侧胸大肌和腹直肌肌皮瓣完成覆盖。术中组织扩张将缺损手术重建产生的心脏压迫降至最低。我们的患者现在36个月大，是成功进行重建手术存活下来的第17例病例。
