Smirnov M D, Triplett D T, Comp P C, Esmon N L, Esmon C T
Cardiovascular Biology Research Program, Oklahoma Medical Research Foundation, Oklahoma City 73104.
J Clin Invest. 1995 Jan;95(1):309-16. doi: 10.1172/JCI117657.
Phosphatidylethanolamine (PE) is an important membrane component for supporting activated protein C anticoagulant activity but has little influence on prothrombin activation. This difference constitutes a potential mechanism for selective inhibition of the protein C anticoagulant pathway by lupus anticoagulants and/or antiphospholipid antibodies. In this study, we demonstrate that the presence of PE augments lupus anticoagulant activity. In the plasma of some patients with lupus anticoagulants, activated protein C anticoagulant activity is more potently inhibited than prothrombin activation. As a result, in the presence of activated protein C and PE, these patient plasmas clot faster than normal plasma. Patients with minimal lupus anticoagulant activity are identified whose plasma potently inhibits activated protein C anticoagulant activity. This process is also PE dependent. In three patient plasmas, these phenomena are shown to be due to immunoglobulins. The PE requirement in the expression of activated protein C anticoagulant activity and the PE dependence of some antiphospholipid antibodies provide a mechanistic basis for the selective inhibition of the protein C pathway. Inhibition of activated protein C function may be a common mechanism contributing to increased thrombotic risk in certain patients with antiphospholipid antibodies.
磷脂酰乙醇胺(PE)是支持活化蛋白C抗凝活性的重要膜成分,但对凝血酶原激活影响很小。这种差异构成了狼疮抗凝物和/或抗磷脂抗体选择性抑制蛋白C抗凝途径的潜在机制。在本研究中,我们证明PE的存在增强了狼疮抗凝活性。在一些狼疮抗凝物患者的血浆中,活化蛋白C抗凝活性比凝血酶原激活受到更有效的抑制。因此,在存在活化蛋白C和PE的情况下,这些患者血浆的凝血速度比正常血浆更快。已鉴定出狼疮抗凝活性极低的患者,其血浆能有效抑制活化蛋白C抗凝活性。这一过程也是PE依赖性的。在三例患者血浆中,这些现象被证明是由免疫球蛋白引起的。活化蛋白C抗凝活性表达中的PE需求以及某些抗磷脂抗体的PE依赖性为蛋白C途径的选择性抑制提供了机制基础。抑制活化蛋白C功能可能是导致某些抗磷脂抗体患者血栓形成风险增加的常见机制。