Fujimura Y, Kimura F, Ishida S, Shinoda K, Ohsawa N
First Department of Internal Medicine, Osaka Medical College.
Rinsho Shinkeigaku. 1994 Sep;34(9):918-21.
A 23-year-old man developed slowly progressive muscle weakness from the age of 10, followed by paresthesia and urinary disturbance. The physical examination showed bilateral muscular atrophy in the lower limbs and dissociated sensory disturbance below Th8. Although there was normal appearance of spinal X-P, MRI revealed conus medullaris at S2 involved thoraco-lumbar syringomyelia with extramedullary lipoma. After the operation for laminectomy of L5-S2 and untethering without direct surgery for syringomyelia, post-operated MRI exhibited definite shrinkage of the syrinx. It suggested that thoraco-lumbar syringomyelia in the present case was not congenital anomaly, but secondary outcome to tethered cord syndrome.
一名23岁男性自10岁起出现缓慢进展的肌肉无力,随后出现感觉异常和排尿障碍。体格检查显示双下肢肌肉萎缩,T8以下分离性感觉障碍。虽然脊柱X线平片外观正常,但MRI显示脊髓圆锥位于S2,伴有胸腰段脊髓空洞症和髓外脂肪瘤。在进行L5 - S2椎板切除术和脊髓松解术(未直接对脊髓空洞症进行手术)后,术后MRI显示脊髓空洞明显缩小。这表明本例胸腰段脊髓空洞症并非先天性异常,而是脊髓栓系综合征的继发性结果。