Yamamura A, Niwa J, Hashi K, Nakamura T
Department of Neurosurgery, Sapporo Medical College.
No Shinkei Geka. 1989 Jan;17(1):69-73.
A 47-year-old female was admitted with complaints of spontaneous pain at the medial surface of the right thigh, and worsening of urinary incontinence and weakness of the legs. These phenomena had been noticed previously 20 years ago, and again 10 years ago, respectively. There was a scar like skin abnormality of 4 X 6 cm over the lumbosacral region. Compression on this region induced neuralgic pain around the anus radiating down to both legs. Neurologically, weakness of the legs, sensory impairment on the L2-S5 dermatomes and urinary incontinence were recognized. Plain X-P revealed spina bifida on the lower lumber and sacral vertebrae (L4-S1), where a low density mass was found by spinal CT. Metrizamide CT myelography and MRI disclosed medullaris to be low and the spinal cord to be elongated. There was a meningocele surrounded by subcutaneous lipoma at the caudal end of the spinal cord at L5 level. Upon operation, a meningocele containing neural elements and adherent to the intra and extra-dural lipoma was found protruding through the laminar defect. Lipoma was removed partially. The conus medullaris and cauda equina were freed from the surrounding tissue. Dural plasty using the Lyodura was made. Postoperatively, the pain disappeared and her gait disturbance and sensory impairment were significantly improved, but urinary incontinence remained unchanged. Fifty-six cases of tethered cord syndrome of adult onset were reviewed from the literatures. Clinical symptoms, etiologies of the tethering, surgical outcomes and factors causing symptoms were discussed.(ABSTRACT TRUNCATED AT 250 WORDS)
一名47岁女性因右大腿内侧自发疼痛、尿失禁加重及腿部无力而入院。这些症状分别在20年前和10年前曾被注意到。腰骶部有一处4×6 cm的瘢痕样皮肤异常。对该区域施压会诱发肛门周围神经痛并向下放射至双腿。神经系统检查发现腿部无力、L2 - S5皮节感觉障碍及尿失禁。X线平片显示下腰椎和骶椎(L4 - S1)有脊柱裂,脊髓CT发现低密度肿块。甲泛葡胺CT脊髓造影和MRI显示脊髓圆锥低位且脊髓拉长。在L5水平脊髓尾端有一个被皮下脂肪瘤包绕的脊膜膨出。手术中发现一个包含神经成分且与硬膜内、外脂肪瘤粘连的脊膜膨出经椎板缺损处突出。部分切除脂肪瘤。游离脊髓圆锥和马尾与周围组织的粘连。用Lyodura进行硬脑膜成形术。术后疼痛消失,步态障碍和感觉障碍明显改善,但尿失禁无变化。从文献中回顾了56例成人起病的脊髓拴系综合征病例。讨论了临床症状、拴系病因、手术结果及导致症状的因素。(摘要截选于250词)