Bates D G, Lebowitz R L
Department of Radiology, Children's Hospital, Boston, MA 02115.
Radiology. 1995 Feb;194(2):501-4. doi: 10.1148/radiology.194.2.7824732.
To characterize the radiographic appearances of congenital urethroperineal fistula and to distinguish it from urethral duplication of the hypospadiac type.
The authors examined four patients with congenital urethroperineal fistula in whom radiographic examinations were performed to define the pathologic anatomy.
Congenital urethroperineal fistula mimics the hypospadiac form of urethral duplication, except the normally positioned dorsal channel is the normal urethra. Patients with congenital urethroperineal fistula have normal micturition. Both a normal dorsal penile urethra and a ventral urethroperineal fistula can be observed during radiographic and cystoscopic examination. The dorsal urethra is the functionally normal channel. Excision of the ventral channel is simple and curative. This contrasts starkly with congenital urethral duplication of the hypospadiac type, where excision of the ventral channel may be catastrophic.
Although it resembles the hypospadiac form of urethral duplication, congenital urethroperineal fistula should be classified as a separate entity.
描述先天性尿道会阴瘘的影像学表现，并将其与尿道下裂型尿道重复畸形相鉴别。
作者对4例先天性尿道会阴瘘患者进行了检查，通过影像学检查来明确病理解剖结构。
先天性尿道会阴瘘类似于尿道下裂型尿道重复畸形，不同之处在于正常位置的背侧通道是正常尿道。先天性尿道会阴瘘患者排尿正常。在影像学和膀胱镜检查中均可观察到正常的阴茎背侧尿道和腹侧尿道会阴瘘。背侧尿道是功能正常的通道。切除腹侧通道简单且可治愈。这与尿道下裂型先天性尿道重复畸形形成鲜明对比，后者切除腹侧通道可能带来灾难性后果。
尽管先天性尿道会阴瘘类似于尿道下裂型尿道重复畸形，但应将其归类为一个独立的疾病实体。
