von den Driesch P, Mielke V, Simon M, Staib G, Tacke J, Sterry W
Dermatologische Universitätsklinik, Erlangen.
Hautarzt. 1994 Dec;45(12):861-5. doi: 10.1007/s001050050187.
The term "granulomatous slack skin" (GSS) was introduced by Ackerman for a disease first described by Convit et al. in 1973. GSS represents a rare cutaneous lymphoma characterized by localized elastolytic lesions with a granulomatous infiltrate. We recently observed two male patients with the characteristic features of this disease. Both patients responded well to therapy with interferon-alpha 2b. In one patient clinical remission was stable under long-term treatment with clofazimine. We report on common features of these two patients and give a review of the cases published in the literature.
“肉芽肿性皮肤松弛症”(GSS)这一术语由阿克曼提出,用于描述一种最初由康维特等人于1973年描述的疾病。GSS是一种罕见的皮肤淋巴瘤,其特征为伴有肉芽肿浸润的局限性弹性组织溶解性病变。我们最近观察到两名具有该疾病特征的男性患者。两名患者对α-2b干扰素治疗反应良好。在一名患者中,长期使用氯法齐明治疗后临床缓解情况稳定。我们报告这两名患者的共同特征,并对文献中发表的病例进行综述。