Rollé F, Roger D, Bedane C, Aldigier J C, Serhal C, Bonnetblanc J M, Laskar M
Service de Chirurgie Cardiovasculaire, Hôpital Dupuytren, Limoges.
J Mal Vasc. 1994;19(4):323-5.
The association of Ehlers-Danlos type IV syndrome and acrogeria with renovascular hypertension is reported. Ultrastructural abnormalities observed in our case were different of those associated with acrogeria. We propose that acrogeria associated with Ehlers-Danlos type IV syndrome be a different disease of acrogeria of Gottron. The occurrence of renovascular hypertension in Ehlers-Danlos is unusual.
报告了埃勒斯-当洛综合征IV型和肢端早老症与肾血管性高血压的关联。我们病例中观察到的超微结构异常与肢端早老症相关的异常不同。我们提出，与埃勒斯-当洛综合征IV型相关的肢端早老症是一种不同于戈特龙肢端早老症的疾病。埃勒斯-当洛综合征中肾血管性高血压的发生并不常见。
