Umaña H R, Watier E, Pailheret J P
Service de Chirurgie Plastique, Reconstructrice et Esthétique, Hôpital Sud, Rennes.
Ann Chir Plast Esthet. 1994 Feb;39(1):27-36.
The congenital absence of the vagina has a low incidency but it is a very invalidating condition. The Mayer-Rokitansky-Küster-Hauser syndrome represents 90% of all cases of vaginal aplasia. The authors review the anatomical classification, etiopathogenesis, epidemiology, diagnosis and treatment. Between 1981 and 1991, four cases were treated by recto-vesical dissection and split thickness skin graft technique with adjustable stent. The results are good and correspond to those of the literature. Their quality and duration depend on maintaining the stent for a sufficient length of time. Frequent post-operative follow-up is necessary to prevent graft retraction and to give psychological support when it is needed.
先天性无阴道发病率低,但却是一种使人严重致残的病症。迈耶-罗基坦斯基-库斯特-豪泽综合征占所有阴道发育不全病例的90%。作者回顾了其解剖学分类、病因发病机制、流行病学、诊断和治疗方法。1981年至1991年间,4例患者采用直肠膀胱分离术及带可调节支架的中厚皮片移植技术进行治疗。结果良好,与文献报道相符。其效果和持续时间取决于支架维持足够长的时间。术后需要频繁随访,以防止移植皮片回缩,并在需要时给予心理支持。