Tsuda H, Matsumoto M, Imanaka M, Ogita S
Department of Obstetrics and Gynecology, Osaka City General Hospital, Japan.
Prenat Diagn. 1994 Nov;14(11):1083-5. doi: 10.1002/pd.1970141113.
It is generally recognized that the sonographic findings of infantile polycystic kidney disease (IPKD) are bilaterally enlarged kidneys, oligohydramnios, an absent fetal bladder, and the typical kidney texture. Since there is a broad spectrum of renal compromise with IPKD, in utero diagnosis is thought to be limited to the severe forms. This paper reports a mild case of IPKD, where the in utero diagnosis was established by measuring fetal urine production and amniotic fluid volume serially during pregnancy, and by ultrasonographic examination of fetal kidneys.
一般认为,婴儿型多囊肾病(IPKD)的超声检查结果为双侧肾脏增大、羊水过少、胎儿膀胱缺如以及典型的肾脏质地。由于IPKD存在广泛的肾脏损害范围,宫内诊断被认为仅限于严重形式。本文报告了一例轻度IPKD病例,该病例通过在孕期连续测量胎儿尿量和羊水量以及对胎儿肾脏进行超声检查而得以在宫内确诊。