Tison T, Vianello F, Radossi P, Girolami A, Sgarabotto D, Dazzi F
Istituto di Semeiotica, IV Cattedra di Medicina Interna, Università di Padova, Italy.
Haematologica. 1994 Nov-Dec;79(6):534-5.
We describe a case characterized by the onset of bone marrow hypoplasia. After treatment with steroid and anabolic compounds, it evolved into a myelodysplastic syndrome (MDS) as demonstrated by morphological and karyotypic analysis. Despite the dysplastic nature of the disorder, a unique feature was its association with a high platelet count. The pathogenesis of the thrombocytosis could not be clearly identified. In fact, the course of the disease was complicated by severe infections that, together with therapy, could have played some role in stimulating thrombopoiesis. However, since MDS can precede or follow a chronic myeloproliferative disease, it is also possible that the platelet elevation in our patient could have been sustained by a primitive thrombocyte disorder.
我们描述了一例以骨髓发育不全起病为特征的病例。经类固醇和合成代谢化合物治疗后,经形态学和核型分析证实其演变为骨髓增生异常综合征(MDS)。尽管该疾病具有发育异常的性质,但其一个独特特征是与血小板计数升高有关。血小板增多症的发病机制尚不能明确。实际上,疾病过程因严重感染而复杂化,这些感染与治疗一起可能在刺激血小板生成中发挥了一定作用。然而,由于MDS可先于或继发于慢性骨髓增殖性疾病,因此我们患者的血小板升高也有可能是由原发性血小板疾病维持的。