Peng H C, Chen H C, Chang W T
Department of Surgery, Taichung Veterans General Hospital, Taiwan, R.O.C.
J Formos Med Assoc. 1993 Aug;92(8):762-4.
Three cases are presented in which the recognized syndrome of functional small bowel obstruction with malrotation and short small bowel was diagnosed. Each patient underwent an exploratory laparotomy for intestinal obstruction, which revealed short small intestines with malrotation, measuring 30 cm to 39 cm. Ladd's procedure was performed in each case and gastrointestinal patency was assured during the operations. Two patients received long-term parenteral nutrition and one, in addition, received bowel lengthening using Bianchi's method. However, the symptoms persisted. The third patient received a prokinetic agent (cisapride) but with no effect; the parents withdrew further management. All three patients subsequently died. Although autopsies were performed in two cases, the exact deficits of intestinal motility are unknown.
本文报告了3例诊断为功能性小肠梗阻合并肠旋转不良和短小肠综合征的病例。每位患者均因肠梗阻接受了剖腹探查术，术中发现小肠短且伴有肠旋转不良，长度为30 cm至39 cm。每例均行Ladd手术，术中确保胃肠道通畅。2例患者接受了长期肠外营养，其中1例还采用Bianchi法进行了肠延长术。然而，症状持续存在。第3例患者接受了促动力药（西沙必利）治疗，但无效；其父母放弃了进一步治疗。所有3例患者随后均死亡。尽管其中2例行尸检，但确切的肠道动力缺陷尚不清楚。
