Nine J S, Yousem S A, Paradis I L, Keenan R, Griffith B P
Department of Pathology, University of Pittsburgh Medical Center, PA 15213.
J Heart Lung Transplant. 1994 Jul-Aug;13(4):714-9.
Pulmonary lymphangioleiomyomatosis is a disease principally affecting women during child-bearing years that eventually leads to respiratory failure. Recently, it has been listed as an indication for lung transplantation. To date, no cases of recurrent lymphangioleiomyomatosis after lung transplantation have been reported, unlike the experience with sarcoidosis and giant cell interstitial pneumonia. At the University of Pittsburgh Medical Center, four patients have undergone single-lung transplantation for lymphangioleiomyomatosis. We now report that one of these cases developed recurrent lymphangioleiomyomatosis in the allograft lung.
肺淋巴管平滑肌瘤病是一种主要影响育龄期女性的疾病，最终会导致呼吸衰竭。最近，它已被列为肺移植的适应证。迄今为止，与结节病和巨细胞间质性肺炎的情况不同，尚无肺移植后复发性淋巴管平滑肌瘤病的病例报道。在匹兹堡大学医学中心，有4例患者因淋巴管平滑肌瘤病接受了单肺移植。我们现在报告其中1例患者在移植肺中出现了复发性淋巴管平滑肌瘤病。
